Congenital choledochal cyst with intrahepatic involvement
T. Todani, Y. Watanabe, T. Fujii, A. Toki, S. Uemura and Y. Koike
We reviewed congenital choledochal cyst with intrahepatic involvement in 38
patients aged 52 days to 29 years. Dilatations were classified into the
following three forms, based on the shape of the extrahepatic and
intrahepatic bile duct: cystic-cystic, cystic-cylindrical, and
cylindrical-cylindrical. Stenosis of the hepatic duct near the hilum
probably does not cause dilatation of the intrahepatic duct. The anomalous
arrangement of the pancreatobiliary union seems to determine only the form
of extrahepatic dilatation, and cystic dilatation of the intrahepatic duct
may be caused by some other factors. Total excision of the extrahepatic
bile duct with the creation of a wide anastomotic stoma apparently is the
treatment of choice. Hepatectomy would be recommended for some patients
with the cystic-cystic form.
